{"id":801,"date":"2019-04-04T07:48:20","date_gmt":"2019-04-04T07:48:20","guid":{"rendered":"http:\/\/diamnd-blackfan-ev-ansicht.advosbrand.de\/?page_id=801"},"modified":"2020-03-10T12:33:36","modified_gmt":"2020-03-10T12:33:36","slug":"ursachen","status":"publish","type":"page","link":"https:\/\/diamond-blackfan.de\/?page_id=801","title":{"rendered":"Ursachen"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-post\" data-elementor-id=\"801\" class=\"elementor elementor-801\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-93c725c elementor-section-stretched elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"93c725c\" data-element_type=\"section\" data-settings=\"{&quot;stretch_section&quot;:&quot;section-stretched&quot;,&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4654709\" data-id=\"4654709\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-392dee8 elementor-widget__width-auto elementor-widget elementor-widget-heading\" data-id=\"392dee8\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Diamond - Blackfan \u2013 An\u00e4mie<br \/><\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2219a56 elementor-widget elementor-widget-spacer\" data-id=\"2219a56\" data-element_type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2a7ddf7 elementor-widget__width-auto elementor-widget elementor-widget-heading\" data-id=\"2a7ddf7\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\"><strong>INFOS ZUR KRANKHEIT<\/strong><\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-b85210a elementor-align-left elementor-widget elementor-widget-button\" data-id=\"b85210a\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-md\" href=\"?page_id=822\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t<span class=\"elementor-button-icon\">\n\t\t\t\t\t\t\t\t\t<i class=\"fa fa-long-arrow-right\" aria-hidden=\"true\"><\/i>\n\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Spenden &amp; helfen<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-78722dc elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"78722dc\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-66 elementor-top-column elementor-element elementor-element-83a0925\" data-id=\"83a0925\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2df3588 elementor-widget elementor-widget-heading\" data-id=\"2df3588\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-large\">Ursache<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5cfc166 elementor-widget elementor-widget-text-editor\" data-id=\"5cfc166\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div>Die Diamond &#8211; Blackfan \u2014 An\u00e4mie\u200e (DBA) ist eine Erkrankung, die von einem Elternteil vererbt sein kann. Sie kann aber auch durch eine spontane Genver\u00e4nderung (Neumutation) beim Patienten zum ersten Mal auftreten und sich sp\u00e4ter weitervererben. Die Diamond-Blackfan-An\u00e4mie (DBA) ist nicht ansteckend und kann auch nicht im Laufe des Lebens erworben werden.<\/div><div>\u00a0<\/div><div>Die DBA wird durch Fehler (Mutation\u200een) in den Erbanlagen (Gen\u200ee) verursacht, die f\u00fcr die Produktion bestimmter Eiwei\u00dfe (Proteine) zust\u00e4ndig sind. Dadurch kommt es zur Produktion fehlerhafter Proteine. Diese Proteine sind die Grundbausteine der &#8222;Eiwei\u00dffabriken&#8220; in den K\u00f6rperzellen, den Ribosomen. Ribosomen befinden sich im Zellkern einer Zelle.<\/div><div>\u00a0<\/div><div>Warum dies geschieht ist unbekannt. Inzwischen wurden mehrere Gene entdeckt, die Ver\u00e4nderungen aufweisen \u2013 aber nicht bei allen Erkrankten und nicht einheitlich.<\/div>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-709a3ef\" data-id=\"709a3ef\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ff699b2 elementor-widget elementor-widget-image\" data-id=\"ff699b2\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<a href=\"http:\/\/www.shopplusplus.de\/diamond-blackfan\" target=\"_blank\">\n\t\t\t\t\t\t\t<img decoding=\"async\" width=\"151\" height=\"100\" src=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2019\/04\/Shoppenhilft_Verein_151x100.png\" class=\"attachment-large size-large wp-image-948\" alt=\"\" srcset=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2019\/04\/Shoppenhilft_Verein_151x100.png 151w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2019\/04\/Shoppenhilft_Verein_151x100-150x100.png 150w\" sizes=\"(max-width: 151px) 100vw, 151px\" \/>\t\t\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2a1fab6 elementor-widget elementor-widget-html\" data-id=\"2a1fab6\" data-element_type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div style=\"text-align:center\"><form action=\"https:\/\/www.paypal.com\/cgi-bin\/webscr\" method=\"post\" target=\"_top\">\r\n\r\n<input type=\"hidden\" name=\"cmd\" value=\"_s-xclick\" \/>\r\n\r\n<input type=\"hidden\" name=\"hosted_button_id\" value=\"7DVELAUQXDSR6\" \/>\r\n\r\n<input type=\"image\" src=\"https:\/\/www.paypalobjects.com\/de_DE\/DE\/i\/btn\/btn_donateCC_LG.gif\" border=\"0\" name=\"submit\" title=\"PayPal - The safer, easier way to pay online!\" alt=\"Spenden mit dem PayPal-Button\" \/>\r\n\r\n<img decoding=\"async\" alt=\"\" border=\"0\" src=\"https:\/\/www.paypal.com\/de_DE\/i\/scr\/pixel.gif\" width=\"1\" height=\"1\" \/>\r\n\r\n<\/form>\r\n<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-622b799 elementor-widget elementor-widget-html\" data-id=\"622b799\" data-element_type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\n\n<div class=\"su-posts su-posts-default-loop \">\n\n\t\n\t\t\t\t\t\n\t\t\t\n\t\t\t<div id=\"su-post-1925\" class=\"su-post \">\n\n\t\t\t\t\t\t\t\t\t<a class=\"su-post-thumbnail\" href=\"https:\/\/diamond-blackfan.de\/?p=1925\"><img fetchpriority=\"high\" decoding=\"async\" width=\"1278\" height=\"719\" src=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video.jpg\" class=\"attachment-post-thumbnail size-post-thumbnail wp-post-image\" alt=\"\" srcset=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video.jpg 1278w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video-300x169.jpg 300w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video-1024x576.jpg 1024w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video-768x432.jpg 768w\" sizes=\"(max-width: 1278px) 100vw, 1278px\" \/><\/a>\n\t\t\t\t\n\t\t\t\t<h2 class=\"su-post-title\"><a href=\"https:\/\/diamond-blackfan.de\/?p=1925\">Diamond &#8211; Blackfan &#8211; An\u00e4mie Selbsthilfe Deutschland e.V.<\/a><\/h2>\n\n\t\t\t\t<div class=\"su-post-meta\">\n\t\t\t\t\tVer\u00f6ffentlicht: Oktober 21, 2023\t\t\t\t<\/div>\n\n\t\t\t\t<div class=\"su-post-excerpt\">\n\t\t\t\t\t\t\t\t\t<\/div>\n\n\t\t\t\t\n\t\t\t<\/div>\n\n\t\t\t\t\t\n\t\t\t\n\t\t\t<div id=\"su-post-1806\" class=\"su-post \">\n\n\t\t\t\t\t\t\t\t\t<a class=\"su-post-thumbnail\" href=\"https:\/\/diamond-blackfan.de\/?p=1806\"><img loading=\"lazy\" decoding=\"async\" width=\"806\" height=\"453\" src=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv.jpg\" class=\"attachment-post-thumbnail size-post-thumbnail wp-post-image\" alt=\"\" srcset=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv.jpg 806w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv-300x169.jpg 300w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv-768x432.jpg 768w\" sizes=\"(max-width: 806px) 100vw, 806px\" \/><\/a>\n\t\t\t\t\n\t\t\t\t<h2 class=\"su-post-title\"><a href=\"https:\/\/diamond-blackfan.de\/?p=1806\">Rare Disease Day<\/a><\/h2>\n\n\t\t\t\t<div class=\"su-post-meta\">\n\t\t\t\t\tVer\u00f6ffentlicht: November 9, 2021\t\t\t\t<\/div>\n\n\t\t\t\t<div class=\"su-post-excerpt\">\n\t\t\t\t\t\t\t\t\t<\/div>\n\n\t\t\t\t\n\t\t\t<\/div>\n\n\t\t\n\t\n<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Diamond &#8211; Blackfan \u2013 An\u00e4mie INFOS ZUR KRANKHEIT Spenden &amp; helfen Ursache Die Diamond &#8211; Blackfan \u2014 An\u00e4mie\u200e (DBA) ist eine Erkrankung, die von einem Elternteil vererbt sein kann. Sie kann aber auch durch eine spontane Genver\u00e4nderung (Neumutation) beim Patienten zum ersten Mal auftreten und sich sp\u00e4ter weitervererben. Die Diamond-Blackfan-An\u00e4mie (DBA) ist nicht ansteckend und [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"elementor_header_footer","meta":{"zakra_sidebar_layout":"customizer","zakra_remove_content_margin":false,"zakra_sidebar":"customizer","zakra_transparent_header":"0","zakra_logo":0,"zakra_main_header_style":"default","zakra_menu_item_color":"","zakra_menu_item_hover_color":"","zakra_menu_item_active_color":"","zakra_menu_active_style":"","zakra_page_header":true,"footnotes":""},"class_list":["post-801","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages\/801","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=801"}],"version-history":[{"count":9,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages\/801\/revisions"}],"predecessor-version":[{"id":1590,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages\/801\/revisions\/1590"}],"wp:attachment":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=801"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}