{"id":794,"date":"2019-04-04T07:38:09","date_gmt":"2019-04-04T07:38:09","guid":{"rendered":"http:\/\/diamnd-blackfan-ev-ansicht.advosbrand.de\/?page_id=794"},"modified":"2020-03-10T12:22:55","modified_gmt":"2020-03-10T12:22:55","slug":"krankheitsbild","status":"publish","type":"page","link":"https:\/\/diamond-blackfan.de\/?page_id=794","title":{"rendered":"Krankheitsbild"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-post\" data-elementor-id=\"794\" class=\"elementor elementor-794\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-10f73ba elementor-section-stretched elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"10f73ba\" data-element_type=\"section\" data-settings=\"{&quot;stretch_section&quot;:&quot;section-stretched&quot;,&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-14702ca\" data-id=\"14702ca\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-569a00c elementor-widget__width-auto elementor-widget elementor-widget-heading\" data-id=\"569a00c\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Diamond - Blackfan \u2013 An\u00e4mie<br \/><\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-901ba5b elementor-widget elementor-widget-spacer\" data-id=\"901ba5b\" data-element_type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-159d683 elementor-widget__width-auto elementor-widget elementor-widget-heading\" data-id=\"159d683\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\"><strong>INFOS ZUR KRANKHEIT<\/strong><\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-eb9223f elementor-align-left elementor-widget elementor-widget-button\" data-id=\"eb9223f\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-md\" href=\"?page_id=822\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t<span class=\"elementor-button-icon\">\n\t\t\t\t\t\t\t\t\t<i class=\"fa fa-long-arrow-right\" aria-hidden=\"true\"><\/i>\n\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Spenden &amp; helfen<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d0c44cf elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d0c44cf\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-66 elementor-top-column elementor-element elementor-element-ff6d931\" data-id=\"ff6d931\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b7e6657 elementor-widget elementor-widget-heading\" data-id=\"b7e6657\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-large\">Krankheitsbild<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-48c81e8 elementor-widget elementor-widget-text-editor\" data-id=\"48c81e8\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Die DBA wurde 1938 von den Kinder\u00e4rzten Louis K. Diamond und Kenneth D. Blackfan erstmals beschrieben.<\/p><p>Die Diamond &#8211; Blackfan \u2014 An\u00e4mie (DBA) ist eine angeborene schwere, chronische Blutarmut, bei der die roten Blutzellen im Knochenmark nicht oder nur unzureichend gebildet werden. Sie tritt meistens im 1. Lebensjahr auf und geh\u00f6rt mit 5-7 f\u00e4llen pro 1 Million Neugeborene zu den sehr seltenen Erkrankungen.<\/p><p>Typische Beschwerden von Erkrankten sind unter anderem:<\/p><ul><li>zunehmende Bl\u00e4sse<\/li><li>Herzrasen<\/li><li>Kopfschmerzen<\/li><li>rasche Erm\u00fcdbarkeit<\/li><li>Trinkunlust und Gedeihst\u00f6rungen<\/li><li>Luftnot bei k\u00f6rperlicher Anstrengung<\/li><\/ul><p>Aber auch angeborene Fehlbildungen k\u00f6nnen zum Krankheitsbild geh\u00f6ren.<br \/>Bei etwa 40% der Patienten zeigt sich dies mit:<\/p><ul><li>typisches &#8222;DBA-Gesicht&#8220; mit Stupsnase, breitem Augenabstand (Hypertelorismus), kr\u00e4ftiger Oberlippe und aufgewecktem Gesichtsausdruck<\/li><li>Kleinwuchs<\/li><li>Skelettver\u00e4nderungen (besonders der Arme und\/oder der Daumen)<\/li><li>Gaumenspalte<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-5151748\" data-id=\"5151748\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4b5ce0d elementor-widget elementor-widget-image\" data-id=\"4b5ce0d\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<a href=\"http:\/\/www.shopplusplus.de\/diamond-blackfan\" target=\"_blank\">\n\t\t\t\t\t\t\t<img decoding=\"async\" width=\"151\" height=\"100\" src=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2019\/04\/Shoppenhilft_Verein_151x100.png\" class=\"attachment-large size-large wp-image-948\" alt=\"\" srcset=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2019\/04\/Shoppenhilft_Verein_151x100.png 151w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2019\/04\/Shoppenhilft_Verein_151x100-150x100.png 150w\" sizes=\"(max-width: 151px) 100vw, 151px\" \/>\t\t\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-795ec4d elementor-widget elementor-widget-html\" data-id=\"795ec4d\" data-element_type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<div style=\"text-align:center\"><form action=\"https:\/\/www.paypal.com\/cgi-bin\/webscr\" method=\"post\" target=\"_top\">\r\n\r\n<input type=\"hidden\" name=\"cmd\" value=\"_s-xclick\" \/>\r\n\r\n<input type=\"hidden\" name=\"hosted_button_id\" value=\"7DVELAUQXDSR6\" \/>\r\n\r\n<input type=\"image\" src=\"https:\/\/www.paypalobjects.com\/de_DE\/DE\/i\/btn\/btn_donateCC_LG.gif\" border=\"0\" name=\"submit\" title=\"PayPal - The safer, easier way to pay online!\" alt=\"Spenden mit dem PayPal-Button\" \/>\r\n\r\n<img decoding=\"async\" alt=\"\" border=\"0\" src=\"https:\/\/www.paypal.com\/de_DE\/i\/scr\/pixel.gif\" width=\"1\" height=\"1\" \/>\r\n\r\n<\/form>\r\n<\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7a6488b elementor-widget elementor-widget-html\" data-id=\"7a6488b\" data-element_type=\"widget\" data-widget_type=\"html.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\n\n<div class=\"su-posts su-posts-default-loop \">\n\n\t\n\t\t\t\t\t\n\t\t\t\n\t\t\t<div id=\"su-post-1925\" class=\"su-post \">\n\n\t\t\t\t\t\t\t\t\t<a class=\"su-post-thumbnail\" href=\"https:\/\/diamond-blackfan.de\/?p=1925\"><img fetchpriority=\"high\" decoding=\"async\" width=\"1278\" height=\"719\" src=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video.jpg\" class=\"attachment-post-thumbnail size-post-thumbnail wp-post-image\" alt=\"\" srcset=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video.jpg 1278w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video-300x169.jpg 300w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video-1024x576.jpg 1024w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2023\/10\/kv-video-768x432.jpg 768w\" sizes=\"(max-width: 1278px) 100vw, 1278px\" \/><\/a>\n\t\t\t\t\n\t\t\t\t<h2 class=\"su-post-title\"><a href=\"https:\/\/diamond-blackfan.de\/?p=1925\">Diamond &#8211; Blackfan &#8211; An\u00e4mie Selbsthilfe Deutschland e.V.<\/a><\/h2>\n\n\t\t\t\t<div class=\"su-post-meta\">\n\t\t\t\t\tVer\u00f6ffentlicht: Oktober 21, 2023\t\t\t\t<\/div>\n\n\t\t\t\t<div class=\"su-post-excerpt\">\n\t\t\t\t\t\t\t\t\t<\/div>\n\n\t\t\t\t\n\t\t\t<\/div>\n\n\t\t\t\t\t\n\t\t\t\n\t\t\t<div id=\"su-post-1806\" class=\"su-post \">\n\n\t\t\t\t\t\t\t\t\t<a class=\"su-post-thumbnail\" href=\"https:\/\/diamond-blackfan.de\/?p=1806\"><img loading=\"lazy\" decoding=\"async\" width=\"806\" height=\"453\" src=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv.jpg\" class=\"attachment-post-thumbnail size-post-thumbnail wp-post-image\" alt=\"\" srcset=\"https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv.jpg 806w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv-300x169.jpg 300w, https:\/\/diamond-blackfan.de\/wp-content\/uploads\/2021\/11\/v1prv-768x432.jpg 768w\" sizes=\"(max-width: 806px) 100vw, 806px\" \/><\/a>\n\t\t\t\t\n\t\t\t\t<h2 class=\"su-post-title\"><a href=\"https:\/\/diamond-blackfan.de\/?p=1806\">Rare Disease Day<\/a><\/h2>\n\n\t\t\t\t<div class=\"su-post-meta\">\n\t\t\t\t\tVer\u00f6ffentlicht: November 9, 2021\t\t\t\t<\/div>\n\n\t\t\t\t<div class=\"su-post-excerpt\">\n\t\t\t\t\t\t\t\t\t<\/div>\n\n\t\t\t\t\n\t\t\t<\/div>\n\n\t\t\n\t\n<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-57c85cf elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"57c85cf\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-bbaa2ea\" data-id=\"bbaa2ea\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Diamond &#8211; Blackfan \u2013 An\u00e4mie INFOS ZUR KRANKHEIT Spenden &amp; helfen Krankheitsbild Die DBA wurde 1938 von den Kinder\u00e4rzten Louis K. Diamond und Kenneth D. Blackfan erstmals beschrieben. Die Diamond &#8211; Blackfan \u2014 An\u00e4mie (DBA) ist eine angeborene schwere, chronische Blutarmut, bei der die roten Blutzellen im Knochenmark nicht oder nur unzureichend gebildet werden. Sie [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"elementor_header_footer","meta":{"zakra_sidebar_layout":"customizer","zakra_remove_content_margin":false,"zakra_sidebar":"customizer","zakra_transparent_header":"0","zakra_logo":0,"zakra_main_header_style":"default","zakra_menu_item_color":"","zakra_menu_item_hover_color":"","zakra_menu_item_active_color":"","zakra_menu_active_style":"","zakra_page_header":true,"footnotes":""},"class_list":["post-794","page","type-page","status-publish","hentry"],"_links":{"self":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages\/794","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages"}],"about":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/types\/page"}],"author":[{"embeddable":true,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/users\/1"}],"replies":[{"embeddable":true,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=%2Fwp%2Fv2%2Fcomments&post=794"}],"version-history":[{"count":21,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages\/794\/revisions"}],"predecessor-version":[{"id":1574,"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=\/wp\/v2\/pages\/794\/revisions\/1574"}],"wp:attachment":[{"href":"https:\/\/diamond-blackfan.de\/index.php?rest_route=%2Fwp%2Fv2%2Fmedia&parent=794"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}